The UMD-VHL mutations database
Record ID: 619

Mutation description


Variation name (cDNA level)Variation name (protein level)Variation statusVariation class
c.194C>Tp.Ser65LeuHeterozygous5- Causal

wt codonwt aamutant codonmutant aamutational eventmutation type
TCGSerTTGLeuC->TTs

StructureKey Residue (HCD)Pyrimidin doubletCpG
Coil 1b Yes, coding strandYes

Mutation impact


At the mRNA levelOn restriction map
New restriction site(s): none
Lost restriction site(s): none

Conservation (0-1)SIFT (0-1)UMD-predictor (0-100)
0 - 71 (Probably pathogenous)

Patient and sample data


Sample IDPatient statusGenderTransmissionAge of onsetAge of DeathGeographic origin
VProbandFalseGerm line

Phenotypic groupDisease
Please contact curator

Reference


Reference IDPubMed IDReference
309829912
Olschwang S., Richard S., Boisson C., Giraud S., Puig PL., Resche F., Thomas G. Germline mutation profile of the VHL gene in von Hippel-Lindau disease and in sporadic hemangioblastoma. Hum Mutat. 1998;12(6):424-30.